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    Idiopathic Pulmonary Fibrosis

    Idiopathic Pulmonary Fibrosis

    National Organization for Rare Disorders, Inc.

    Important
    It is possible that the main title of the report Idiopathic Pulmonary Fibrosis is not the name you expected. Please check the synonyms listing to find the alternate name(s) and disorder subdivision(s) covered by this report.

    Synonyms

    • Alveolocapillary block
    • Cryptogenic Fibrosing Alveolitis
    • Diffuse Fibrosing Alveolitis
    • Fibrosing Alveolitis
    • Hamman-Rich Syndrome
    • Interstitial Diffuse Pulmonary Fibrosis

    Disorder Subdivisions

    • None

    General Discussion

    Idiopathic pulmonary fibrosis is an inflammatory lung disorder of unknown origin (idiopathic) characterized by abnormal formation of fibrous tissue (fibrosis) between the tiny air sacs (alveoli) or ducts of the lungs. Coughing and rapid, shallow breathing occur with moderate exercise. The skin may appear slightly bluish (cyanotic) due to lack of circulating oxygen. Complications such as infection, emphysema or heart problems may develop.

    Resources

    Scleroderma Research Foundation
    220 Montgomery Street
    Suite 1411
    San Francisco, CA 94104
    USA
    Tel: (415)834-9444
    Fax: (415)834-9177
    Tel: (800)441-2873
    Email: srfcure@sclerodermaresearch.org
    Internet: http://www.srfcure.org/home

    American Autoimmune Related Diseases Association, Inc.
    22100 Gratiot Ave.
    Eastpointe, MI 48021
    Tel: (586)776-3900
    Fax: (586)776-3903
    Tel: (800)598-4668
    Email: aarda@aarda.org
    Internet: http://www.aarda.org/

    American Lung Association
    1301 Pennsylvania Ave NW
    Suite 800
    Washington, DC 20004
    USA
    Tel: (202)785-3355
    Fax: (202)452-1805
    Tel: (800)586-4872
    Email: info@lungusa.org
    Internet: http://www.lungusa.org

    NIH/National Heart, Lung and Blood Institute
    P.O. Box 30105
    Bethesda, MD 20892-0105
    Tel: (301)592-8573
    Fax: (301)251-1223
    Email: nhlbiinfo@rover.nhlbi.nih.gov
    Internet: http://www.nhlbi.nih.gov/

    Coalition for Pulmonary Fibrosis
    10866 W Washington Blvd Ste 343
    Culver City, CA 90232
    USA
    Tel: (888)222-8541
    Fax: (408)266-3289
    Tel: (888)222-8541
    Email: info@coalitionforpf.org
    Internet: http://www.coalitionforpf.org

    Pulmonary Fibrosis Foundation
    230 East Ohio Street
    Suite 304
    Chicago, IL 60611-3201
    USA
    Fax: (866)587-9158
    Tel: (888)733-6741
    Email: info@pulmonaryfibrosis.org
    Internet: http://www.pulmonaryfibrosis.org

    Genetic and Rare Diseases (GARD) Information Center
    PO Box 8126
    Gaithersburg, MD 20898-8126
    Tel: (301)251-4925
    Fax: (301)251-4911
    Tel: (888)205-2311
    TDD: (888)205-3223
    Internet: http://rarediseases.info.nih.gov/GARD/

    Autoimmune Information Network, Inc.
    PO Box 4121
    Brick, NJ 08723
    Fax: (732)543-7285
    Email: autoimmunehelp@aol.com

    European Society for Immunodeficiencies
    1-3 rue de Chantepoulet
    Geneva, CH 1211
    Switzerland
    Tel: 410229080484
    Fax: 41229069140
    Email: esid@kenes.com
    Internet: http://www.esid.org

    AutoImmunity Community
    Email: moderator@autoimmunitycommunity.org
    Internet: http://www.autoimmunitycommunity.org

    Global Fibrosis Foundation
    5036 Dr. Phillips Boulevard
    Suite 244
    Orlando, FL 32819
    Tel: (407)909-0753
    Fax: (407)909-0153
    Tel: (800)872-6874
    Email: globalfibrosis@gmail.com
    Internet: http://www.globalfibrosis.com

    For a Complete Report

    This is an abstract of a report from the National Organization for Rare Disorders (NORD). A copy of the complete report can be downloaded free from the NORD website for registered users. The complete report contains additional information including symptoms, causes, affected population, related disorders, standard and investigational therapies (if available), and references from medical literature. For a full-text version of this topic, go to www.rarediseases.org and click on Rare Disease Database under "Rare Disease Information".

    The information provided in this report is not intended for diagnostic purposes. It is provided for informational purposes only. NORD recommends that affected individuals seek the advice or counsel of their own personal physicians.

    It is possible that the title of this topic is not the name you selected. Please check the Synonyms listing to find the alternate name(s) and Disorder Subdivision(s) covered by this report

    This disease entry is based upon medical information available through the date at the end of the topic. Since NORD's resources are limited, it is not possible to keep every entry in the Rare Disease Database completely current and accurate. Please check with the agencies listed in the Resources section for the most current information about this disorder.

    For additional information and assistance about rare disorders, please contact the National Organization for Rare Disorders at P.O. Box 1968, Danbury, CT 06813-1968; phone (203) 744-0100; web site www.rarediseases.org or email orphan@rarediseases.org

    Last Updated:  3/16/2007
    Copyright  1987, 1989, 1999, 2000, 2004, 2007 National Organization for Rare Disorders, Inc.

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